Bronchiolitis obliterans organising pneumonia and primary biliary cirrhosis-like lung involvement in a patient with primary biliary cirrhosis
Autor: | E S Strobel, H E Schaefer, R B Bonnet, P Werner, Hans-Hartmut Peter |
---|---|
Rok vydání: | 1998 |
Předmět: |
Pathology
medicine.medical_specialty Antimetabolites Bronchiolitis obliterans Azathioprine Bronchoalveolar Lavage Primary biliary cirrhosis Rheumatology Adrenal Cortex Hormones Biopsy medicine Humans Lung medicine.diagnostic_test Liver Cirrhosis Biliary business.industry Biopsy Needle General Medicine Middle Aged medicine.disease Respiratory Function Tests medicine.anatomical_structure Bronchoalveolar lavage Cryptogenic Organizing Pneumonia Bronchiolitis Drug Therapy Combination Female Crackles medicine.symptom Lung Diseases Interstitial business Follow-Up Studies medicine.drug |
Zdroj: | Clinical Rheumatology. 17:246-249 |
ISSN: | 1434-9949 0770-3198 |
DOI: | 10.1007/bf01451058 |
Popis: | A 55-year-old woman with a 6-year history of primary biliary cirrhosis presented with an acute onset of fever, dyspnoea, crackles over both lower lung fields, and diffuse interstitial and bibasilar patchy pulmonary opacities. After exclusion of an infectious aetiology, an open lung biopsy was performed which revealed two histopathological features: (1) bronchiolitis obliterans organising pneumonia and (2) lympho-histiocytic interstitial pneumonitis and destructive bronchiolitis. Treatment response to corticosteroids and azathioprine followed a bimodal pattern with immediate resolution of her initial presenting symptoms and late resolution of residual gas exchange defects. |
Databáze: | OpenAIRE |
Externí odkaz: |