Reversal of Defective Lysosomal Transport in NPC Disease Ameliorates Liver Dysfunction and Neurodegeneration in the $npc1^{ - / - } $ Mouse

Autor: Liu, Benny, Turley, Stephen D., Burns, Dennis K., Miller, Anna M., Repa, Joyce J., Dietschy, John M., Brown, Michael S.
Zdroj: Proceedings of the National Academy of Sciences of the United States of America, 2009 Feb . 106(7), 2377-2382.
Databáze: JSTOR Journals