Pulmonary delivery of recombinant acid sphingomyelinase improves clearance of lysosomal sphingomyelin from the lungs of a murine model of Niemann–Pick disease

Autor: Ziegler, Robin J., Brown, Claire, Barbon, Christine M., D’Angona, Anne Marie, Schuchman, Edward H., Andrews, Laura, Thurberg, Beth L., McPherson, John M., Karey, Kenneth P., Cheng, Seng H.
Zdroj: In Molecular Genetics and Metabolism 2009 97(1):35-42
Databáze: ScienceDirect