N-butyldeoxygalactonojirimycin reduces brain ganglioside and GM2 content in neonatal Sandhoff disease mice
Autor: | Baek, Rena C., Kasperzyk, Julie L., Platt, Frances M., Seyfried, Thomas N. |
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Zdroj: | In Neurochemistry International 2008 52(6):1125-1133 |
Databáze: | ScienceDirect |
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