N-butyldeoxygalactonojirimycin reduces brain ganglioside and GM2 content in neonatal Sandhoff disease mice

Autor: Baek, Rena C., Kasperzyk, Julie L., Platt, Frances M., Seyfried, Thomas N.
Zdroj: In Neurochemistry International 2008 52(6):1125-1133
Databáze: ScienceDirect