Porphobilinogen deaminase over-expression in hepatocytes, but not in erythrocytes, prevents accumulation of toxic porphyrin precursors in a mouse model of acute intermittent porphyria
Autor: | Unzu, Carmen, Sampedro, Ana, Mauleón, Itsaso, Vanrell, Lucía, Dubrot, Juan, de Salamanca, Rafael Enríquez, González-Aseguinolaza, Gloria, Melero, Ignacio, Prieto, Jesús, Fontanellas, Antonio |
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Zdroj: | In Journal of Hepatology March 2010 52(3):417-424 |
Databáze: | ScienceDirect |
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