Porphobilinogen deaminase over-expression in hepatocytes, but not in erythrocytes, prevents accumulation of toxic porphyrin precursors in a mouse model of acute intermittent porphyria

Autor: Unzu, Carmen, Sampedro, Ana, Mauleón, Itsaso, Vanrell, Lucía, Dubrot, Juan, de Salamanca, Rafael Enríquez, González-Aseguinolaza, Gloria, Melero, Ignacio, Prieto, Jesús, Fontanellas, Antonio
Zdroj: In Journal of Hepatology March 2010 52(3):417-424
Databáze: ScienceDirect