Familial Mediterranean Fever Complicated by a Triad of Adrenal Crisis: Amyloid Goiter and Cardiac Amyloidosis

Autor: Sadi A. Abukhalaf, Beesan W. Dandis, Tasnim Za’tari, Adham M. Amro, Tareq Z. Alzughayyar, Yazan A. Rajabi
Jazyk: angličtina
Rok vydání: 2020
Předmět:
Zdroj: Case Reports in Rheumatology, Vol 2020 (2020)
Druh dokumentu: article
ISSN: 2090-6889
2090-6897
DOI: 10.1155/2020/7865291
Popis: Background. FMF is a common disease in the Mediterranean populations and may be complicated by AA amyloidosis. The coexistence of adrenal and thyroid amyloidosis in AA amyloidosis secondary to familial Mediterranean fever (FMF) is an extremely rare reported condition. We presented a previously unreported triad of adrenal, thyroid, and cardiac amyloidosis secondary to FMF. Presentation of Case. We reported a 23-year-old Palestinian male patient presented with hypotension, vomiting, diarrhea, and abdominal pain. The patient was subsequently diagnosed to have an adrenal crisis with both amyloid goiter and cardiac amyloidosis. Conclusion. It is crucial to recognize the adrenal crisis in patients with AA amyloidosis secondary to FMF who present similarly to acute FMF inflammatory episodes. The adrenal crisis has high morbidity and mortality, especially if not recognized early in the course of the disease.
Databáze: Directory of Open Access Journals
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