Primary epithelioid inflammatory myofibroblastic sarcoma of the brain with fusion mimicking intra-axial glioma: a case report and brief literature review

Autor:	Eric Eunshik Kim, Chul-Kee Park, Koung Mi Kang, Yoonjin Kwak, Sung-Hye Park, Jae-Kyung Won
Jazyk:	English<br />Korean
Rok vydání:	2024
Předmět:	epithelioid inflammatory myofibroblastic sarcoma brain anaplastic lymphoma kinase inflammatory myofibroblastic tumor literature review Pathology RB1-214
Zdroj:	Journal of Pathology and Translational Medicine, Vol 58, Iss 3, Pp 141-145 (2024)
Druh dokumentu:	article
ISSN:	2383-7837 2383-7845
DOI:	10.4132/jptm.2024.04.12
Popis:	An aggressive subtype of inflammatory myofibroblastic tumor, epithelioid inflammatory myofibroblastic sarcoma occurs primarily inside the abdominal cavity, followed by a pulmonary localization. Most harbor anaplastic lymphoma kinase (ALK) gene rearrangements, with RANBP2 and RRBP1 among the well-documented fusion partners. We report the second case of primary epithelioid inflammatory myofibroblastic sarcoma of the brain, with a well-known EML4::ALK fusion. The case is notable for its intra-axial presentation that clinico-radiologically mimicked glioma.
Databáze:	Directory of Open Access Journals
Externí odkaz:	https://doaj.org/article/fbad169d6c6e429eb9ca1da6f26ca747 Zobrazit plný text záznamu View record in DOAJ