Adrenocortical carcinoma in a 6-month-old infant

Autor: Seema Rahar, Devender Singh Chauhan, Shashikant Singh, Arvind Ahuja, Minakshi Bhardwaj, Amita Sen
Jazyk: angličtina
Rok vydání: 2020
Předmět:
Zdroj: Journal of Indian Association of Pediatric Surgeons, Vol 25, Iss 5, Pp 310-313 (2020)
Druh dokumentu: article
ISSN: 0971-9261
1998-3891
61014648
DOI: 10.4103/jiaps.JIAPS_155_19
Popis: Adrenocortical carcinoma (ACC) is a rare malignant tumor arising from the adrenal cortex and it is even rarer in infancy. These tumors are usually hormonally active. We report a case of ACC in a 6-month-old infant who was brought by her mother with complaints of hirsutism and abnormally looking genitalia. Serum 17-alpha-hydroxyprogesterone and serum cortisol levels were raised. Subsequently, imaging studies revealed a large well-circumscribed soft-tissue mass in the right suprarenal region. The tumor was excised, and on histopathology in conjunction with immunohistochemistry, a diagnosis of ACC was given. Only four other cases of ACC have been reported till date in the literature, with an age of 6 months or younger. Hereby, we present a case of ACC in a young infant.
Databáze: Directory of Open Access Journals
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