| Autor: |
David Strauss, Andres Correa, Yulan Gong, Andreas Karachristos, Alexander Kutikov |
| Jazyk: |
angličtina |
| Rok vydání: |
2022 |
| Předmět: |
|
| Zdroj: |
Urology Case Reports, Vol 40, Iss , Pp 101950- (2022) |
| Druh dokumentu: |
article |
| ISSN: |
2214-4420 |
| DOI: |
10.1016/j.eucr.2021.101950 |
| Popis: |
Paragangliomas are rare neuroendocrine tumors that can vary in size and metabolic activity. We report a case of giant bilateral malignant retroperitoneal paragangliomas (PGL) in a patient with germline succinate dehydrogenase B (SDHB) mutation. This patient, who presented in an emaciated and debilitated state, was managed with adrenergic blockade followed by radical primary surgery. After being metabolically and radiographically disease free for 4 years, he underwent salvage resection for recurrent retroperitoneal disease and palliative radiation to a site of solidary vertebral metastasis. We review incidence and prognosis of metastatic PGL. |
| Databáze: |
Directory of Open Access Journals |
| Externí odkaz: |
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