Giant Darier–Ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report

Autor: A. Triki, M. Aloui, M. Ghalleb, I. Jbir, Ben Naceur, J. Ben Hassouna, R. Chargui, K. Rahal
Jazyk: angličtina
Rok vydání: 2021
Předmět:
Zdroj: Journal of Medical Case Reports, Vol 15, Iss 1, Pp 1-4 (2021)
Druh dokumentu: article
ISSN: 1752-1947
DOI: 10.1186/s13256-021-02687-8
Popis: Abstract Background Darier–Ferrand dermatofibrosarcoma (DFS) is a rare malignant cutaneous neoplasm characterized by local aggressiveness, high risk of recurrence, and low metastatic potential. Case presentation A 60-year-old Tunisian man with recurrent abdominopelvic DFS for which he had undergone multiple excisions presented with an extensive DFS that invaded the external genitals. He underwent a large excision with emasculation and thin cutaneous graft of the abdominal wall and local skin flap in the pelvis. Conclusion DFS is a rare yet recurrent skin tumor. Wide excision with free margins remains the cornerstone of treatment. We report a case of a giant DFS treated with wide excision and reconstructive surgery to cover the defect.
Databáze: Directory of Open Access Journals
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