Gorlin-Goltz Syndrome – A Rare Case Entity in Young Child

Autor: Shovita Mondal, Nikil Kumar Jain, Abhishek Dutta, Nishant, Abhijit Dutta, Moushumi Shil, Suman Sen
Jazyk: angličtina
Rok vydání: 2024
Předmět:
Zdroj: Prague Medical Report, Vol 125, Iss 1, Pp 69-78 (2024)
Druh dokumentu: article
ISSN: 2336-2936
1214-6994
23362936
DOI: 10.14712/23362936.2024.7
Popis: Gorlin-Goltz syndrome (GGS) is an infrequent multisystemic disease with an autosomal dominant trait, which depicted presence of numerous basal cell carcinoma in conjunction with multiorgan abnormalities. This syndrome may be diagnosed early by a dentist by routine radiographic exams in the first decade of life, since the keratocystic odontogenic tumour are usually one of the first manifestations of the syndrome. This article includes a case report of the GGS with regard to its history, incidence, etiology, features, investigations, diagnostic criteria, keratocystic odontogenic tumour and treatment modalities.
Databáze: Directory of Open Access Journals