Double outlet right ventricle with anterior and left-sided aorta and subpulmonary ventricular septal defect

Autor: Luciana Braz Peixoto, Samira Morhy Borges Leal, Carlos Eduardo Suaide Silva, Sandra Maria Lima Moreira, Juarez Ortiz
Jazyk: English<br />Portuguese
Rok vydání: 1999
Předmět:
Zdroj: Arquivos Brasileiros de Cardiologia, Vol 73, Iss 5, Pp 446-450 (1999)
Druh dokumentu: article
ISSN: 0066-782X
1678-4170
DOI: 10.1590/S0066-782X1999001100005
Popis: Double outlet right ventricle (DORV) is a heterogeneous group of abnormal ventriculoarterial connections where, by definition, both great arteries (pulmonary artery and aorta) arise primarily from the morphologically right ventricle. This condition affects 1-1.5% of the patients with congenital heart diseases, with a frequency of 1 in each 10,000 live births. We report the case of an 18-day-old infant with DORV and extremely rare anatomical features, such as anterior and left-sided aorta and subpulmonary ventricular septal defect (VSD). In addition to the anatomic features, the role of the echocardiogram for guiding the diagnosis and the surgical therapy of this congenital heart disease are discussed.
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