A case of primary mediastinal Ewing′s sarcoma /primitive neuroectodermal tumor presenting with initial compression of superior vena cava

Autor: Alessia Reali, Gianluca Mortellaro, Simona Allis, Edoardo Trevisiol, Silvia Maria Anglesio, Sara Bartoncini, Maria Grazia Ruo Redda
Jazyk: angličtina
Rok vydání: 2013
Předmět:
Zdroj: Annals of Thoracic Medicine, Vol 8, Iss 2, Pp 121-123 (2013)
Druh dokumentu: article
ISSN: 1817-1737
1998-3557
DOI: 10.4103/1817-1737.109834
Popis: Ewing′s sarcomas and peripheral primitive neuroectodermal tumors (ES/PNETs) are high grade malignant neoplasms. These malignancies are characterized by a chromosome 22 rearrangement, arise from bone or soft tissue, predominantly affect children and young adults, and are grouped in the Ewing family of tumors. Multimodality treatment programs are the treatment of choice. Primary localization of ES/PNET in the mediastinum is extremely rare. We describe a case of ES/PNET presenting as a mediastinal mass with tracheal compression and initial signs of superior vena cava in a 66-year-old woman.
Databáze: Directory of Open Access Journals