| Autor: |
S Dekeyzer, B Houthoofd, A De Potter, M Van Bockstal, P Smeets, D Vogelaers |
| Jazyk: |
angličtina |
| Rok vydání: |
2013 |
| Předmět: |
|
| Zdroj: |
Journal of the Belgian Society of Radiology, Vol 96, Iss 6, Pp 357-359 (2013) |
| Druh dokumentu: |
article |
| ISSN: |
2514-8281 |
| DOI: |
10.5334/jbr-btr.457 |
| Popis: |
Klippel-Trénaunay syndrome is a rare disorder characterized by a triad of port-wine stains, varicose veins, and bony and soft tissue hypertrophy usually involving an extremity. Visceral involvement in Klippel-Trénaunay syndrome is rare, but has been described in the colon, small bowel, bladder, kidney, spleen, liver, mediastinum and brain. In this paper we present the case of a 45-year-old woman with Klippel-Trénaunay syndrome in whom routine physical examination unexpectedly revealed the presence of a left upper quadrant mass. Abdominal US, contrast enhanced CT and whole-body PET-CT demonstrated multiple large cystic lesions within a massively enlarged spleen. Based on the clinical history and imaging findings diffuse hemangiomatosis of the spleen was suspected. This diagnosis was confirmed by pathologic examination after splenectomy. |
| Databáze: |
Directory of Open Access Journals |
| Externí odkaz: |
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