Diagnosis and management of patients with pheochromocytoma/paraganglioma: Consensus of experts of the Russian Medical Society for Arterial Hypertension and the Multidisciplinary Group for the Diagnosis and Treatment of Neuroendocrine Tumors
Autor: | Nataliya V. Blinova, Irena A. Ilovayskaya, Novella M. Chikhladze, Anna Yu. Lugovskaya, Timur A. Britvin, Larisa E. Gurevich, Lidia N. Nefedova, Valentina E. Shikina, Irina E. Chazova |
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Jazyk: | ruština |
Rok vydání: | 2024 |
Předmět: | |
Zdroj: | Терапевтический архив, Vol 96, Iss 7, Pp 645-658 (2024) |
Druh dokumentu: | article |
ISSN: | 0040-3660 2309-5342 00403660 |
DOI: | 10.26442/00403660.2024.07.202779 |
Popis: | The understanding of the nature of catecholamine-secreting tumors has changed significantly in recent years, affecting terminology and classification. Phaeochromocytoma/paraganglioma (PCC/PG) is a rare neuroendocrine tumor from chromaffin tissue that produces and secretes catecholamines. The incidence of PCC/PG is relatively low, with 2–8 cases per 1 million population per year; among patients with arterial hypertension, their prevalence is 0.2–0.6%. However, delayed diagnosis of PCC/PG is associated with a high risk of cardiovascular complications and a high mortality rate. The consensus presents the clinical manifestations of the disease with an emphasis on the course of arterial hypertension as the most common symptom in PCC/PG; modern ideas about the features of diagnosis, aspects of preoperative preparation, treatment, and follow-up of patients with PCC/PG are considered. |
Databáze: | Directory of Open Access Journals |
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