| Autor: |
Hiroshi Kobayashi, Masaaki Uehara, Aya Oda, Erika Matsubara, Hiroyuki Baba, Ryo Matsumiya, Noritada Yoshikawa, Osamu Hosono, Hirotoshi Tanaka |
| Jazyk: |
angličtina |
| Rok vydání: |
2016 |
| Předmět: |
|
| Zdroj: |
Interdisciplinary Neurosurgery, Vol 5, Iss C, Pp 1-2 (2016) |
| Druh dokumentu: |
article |
| ISSN: |
2214-7519 |
| DOI: |
10.1016/j.inat.2016.03.009 |
| Popis: |
We report a 75-year-old man with glucocorticoid-responsive normal pressure hydrocephalus (NPH) complicated with tubulointerstitial renal disease, protein-losing gastroenteropathy (PLG) and elevated serum IgG4, which might be a possible subset of IgG4-related disease (IgG4-RD). Although either PLG or NPH, especially in combination, has rarely been reported in IgG4-RD, the glucocorticoid-responsive nature of every abnormality observed in the patient supports the diagnosis of IgG4-RD. Of course, pathological confirmation is essential to fulfill the recently raised diagnostic criteria, however, such invasive procedure might not always be indicated in high-risk patients. Our report illustrates that IgG4-RD might be considered as one of the underlying causes and/or the aggravating factors of NPH before shunt operation. |
| Databáze: |
Directory of Open Access Journals |
| Externí odkaz: |
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