Rare neuroendocrine tumor decades after bladder exstrophy repair with enterocystoplasty

Autor: Sabine Roux, Marie-Laurence Poli-Merol, Nicolas Merzeau, Stéphane Larré, Priscilla Leon
Jazyk: angličtina
Rok vydání: 2018
Předmět:
Zdroj: Journal of Pediatric Surgery Case Reports, Vol 31, Iss , Pp 10-12 (2018)
Druh dokumentu: article
ISSN: 2213-5766
DOI: 10.1016/j.epsc.2017.11.018
Popis: Bladder exstrophy is associated with an increased risk of bladder cancer. Adenocarcinoma is the main histological type found in the bladder exstrophy, accounting for 95% of cases, whereas squamous cell carcinoma accounts for 3–5% cases. We present here the rare case of the development of a metastatic neuroendocrine tumor on a bladder exstrophy, 26 years after enterocystoplasty enlargement. We describe the presentation of the cancer and the results after treatment by surgery and chemotherapy. Keywords: Bladder exstrophy, Neuroendocrine carcinoma, Urinary bladder neoplasms
Databáze: Directory of Open Access Journals