A rare and curable cause of cyanosis – Congenital portosystemic shunts

Autor: Balasubramaniyan Amirtha Ganesh, Arumugam Aashish, Selvaraj Karthikeyan, Srinivasan Giridharan
Jazyk: angličtina
Rok vydání: 2021
Předmět:
Zdroj: Journal of Clinical and Preventive Cardiology, Vol 10, Iss 1, Pp 42-44 (2021)
Druh dokumentu: article
ISSN: 2250-3528
DOI: 10.4103/JCPC.JCPC_50_20
Popis: Congenital portosystemic shunts (CPSSs) are rare developmental vascular anomalies which are classified into extrahepatic and intrahepatic malformations. Here, we report a 7-year-old girl who presented with a history of progressive dyspnea, pandigital cyanosis, and clubbing. On evaluation, she was found to have a rare combination of both type II extrahepatic and intrahepatic portosystemic shunts which were closed endovascularly in the same setting. Diagnosis of CPSS needs a very high index of clinical suspicion. Timely diagnosis with specific imaging modalities will help in deciding the treatment strategy and may prevent long-term complications.
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