Inflammatory linear verrucous epidermal nevus syndrome with its polymorphic presentation - A rare case report
Autor: | C Anand Kumar, Garima Yeluri, Namita Raghav |
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Jazyk: | angličtina |
Rok vydání: | 2012 |
Předmět: | |
Zdroj: | Contemporary Clinical Dentistry, Vol 3, Iss 1, Pp 119-122 (2012) |
Druh dokumentu: | article |
ISSN: | 0976-237X 0976-2361 |
DOI: | 10.4103/0976-237X.94562 |
Popis: | Epidermal nevi are hamartomatous lesions that are typically present at birth, but can occur anytime during childhood and may rarely appear in adulthood. An estimated one-third of individuals with epidermal nevi have involvement of other organ systems; hence, this condition is considered to be an epidermal nevus syndrome. There are four distinct epidermal nevus syndromes recognizable by the different types of associated epithelial nevi: linear sebaceous nevi, linear nevus comedonicus, linear epidermal nevus, and inflammatory linear verrucous epidermal nevus (ILVEN). Each type may be regarded as a part of a syndrome with other systemic manifestations. We report a rare case of ILVEN syndrome in a 23-year-old female patient with a wide spectrum of mucosal, cutaneous, and skeletal abnormalities, demonstrating the polymorphic presentation of this condition. |
Databáze: | Directory of Open Access Journals |
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