Vogt-Koyanagi-Harada syndrome presenting with encephalopathy

Autor: Alireza E Naeini, Dana Daneshmand, Farzin Khorvash, Ahmad Chitsaz
Jazyk: angličtina
Rok vydání: 2014
Předmět:
Zdroj: Annals of Indian Academy of Neurology, Vol 17, Iss 1, Pp 128-129 (2014)
Druh dokumentu: article
ISSN: 0972-2327
1998-3549
DOI: 10.4103/0972-2327.128585
Popis: Vogt-Koyanagi-Harada (VKH) is a rare syndrome affecting tissues containing melanocytes. The possibility of its autoimmune pathogenesis is supported by high frequent HLA-DR4 presentation, commonly associated with other autoimmune diseases. Eyes are the main affected organs, resulting in blindness. Brain disease is a late-onset event, and is extremely rare. Here, we are reporting a 57-year-old woman, a known case of VKH syndrome, presenting with brain encephalopathy several decades after the initial presentation. We think this long period between initial presentation and presentation of encephalopathy due to VKH syndrome has not been described before. She was treated with corticosteroids and discharged home with a good general condition.
Databáze: Directory of Open Access Journals