Right Lung Agenesis with Tracheal Stenosis due to Complete Tracheal Rings and Postpneumonectomy Like Syndrome Treated with Tissue Expander Placement

Autor:	Yashwant Agrawal, Sandeep Patri, Jagadeesh K. Kalavakunta
Jazyk:	angličtina
Rok vydání:	2016
Předmět:	Diseases of the respiratory system RC705-779
Zdroj:	Case Reports in Pulmonology, Vol 2016 (2016)
Druh dokumentu:	article
ISSN:	2090-6846 2090-6854
DOI:	10.1155/2016/4397641
Popis:	Congenital lung agenesis is an extremely rare condition with an estimated prevalence of 34 in 1,000,000 live births. It is often associated with other congenital malformations of the skeletal, cardiovascular, urogenital, and gastrointestinal systems. We discuss the case of a 5-month-old who presented with increasing stridor over 1 month. Imaging revealed right lung agenesis, complete dextromalposition of heart, and compression of distal trachea. An intrathoracic saline tissue expander was placed which marked improved distal tracheal stenosis. In patients who are symptomatic it becomes imperative to perform surgeries to increase survival as was the case in this patient.
Databáze:	Directory of Open Access Journals
Externí odkaz:	https://doaj.org/article/a990119f1ec54de5abe6cac7f1d4d7c0 Zobrazit plný text záznamu View record in DOAJ Plný text ve formátu PDF