IgG4‐related retroperitoneal fibrosis: A case report of a challenging disease

Autor: Saika Farook, Md. Shariful Alam Jilani, Md. Kamrul Islam, Shamima Rahman, Rumana Ashraf, Naval Mendiratta, Sudhir Kumar Rawal
Jazyk: angličtina
Rok vydání: 2023
Předmět:
Zdroj: Clinical Case Reports, Vol 11, Iss 9, Pp n/a-n/a (2023)
Druh dokumentu: article
ISSN: 2050-0904
DOI: 10.1002/ccr3.7865
Popis: Abstract Immunoglobulin G4 (IgG4)‐related disease (IgG4‐RD) is a multi‐organ immune‐mediated fibroinflammatory disorder that may imitate malignancy, infectious or any other inflammatory disorder. IgG4‐related retroperitoneal fibrosis (IgG4‐RPF) is a rare form of IgG4‐RD, diagnosis of which is often relied on radiological technology. Herein, we describe a case of 60 year old male, presenting with low back pain and weight loss for a period of 2 months and 15 days. Imaging studies showed a retroperitoneal tumorous mass along with bilateral hydroureteronephrosis, which was later confirmed to be IgG4‐related retroperitoneal fibrosis on the basis of extensive histopathological analysis. Immunosuppressive therapy resulted in a decrease in fibrosis and restoration of renal function.
Databáze: Directory of Open Access Journals
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