An Unusual Cause of Hypoxia: Ventricular Septal Defect, Pulmonary Artery Atresia, and Major Aortopulmonary Collaterals Diagnosed in the Adult Cardiac Catheterization Lab

Autor: Katia Bravo-Jaimes, Brian Walton, Poyee Tung, Richard W. Smalling
Jazyk: angličtina
Rok vydání: 2020
Předmět:
Zdroj: Case Reports in Cardiology, Vol 2020 (2020)
Druh dokumentu: article
ISSN: 2090-6404
2090-6412
DOI: 10.1155/2020/4726529
Popis: The association of pulmonary atresia, ventricular septal defect (VSD) and major aortopulmonary collaterals (MAPCA) is an extreme form of tetralogy of Fallot (TOF). It carries a high mortality risk if not intervened on during infancy with only 20% of unoperated patients surviving into adulthood. We present the case of a 40-year-old man who presented for evaluation prior to retinal surgery and was found to have hypoxia and a loud murmur. Cardiac catheterization was performed in the general catheterization laboratory, demonstrating a membranous VSD, pulmonary atresia, and MAPCA. We highlight the challenges and limitations that an adult interventional cardiologist may have when encountering these patients.
Databáze: Directory of Open Access Journals
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