Malignant eccrine spiradenocylindroma and parotid gland involvement in brooke spiegler syndrome

Autor: Giulia Merlo, Marianna Pesce, Tiziana Borra, Ileana Orejuela, Francesca Pasquali, Renzo Panizza, Marco Ghiglione, Federica Grosso
Jazyk: angličtina
Rok vydání: 2022
Předmět:
Zdroj: Dermatology Reports (2022)
Druh dokumentu: article
ISSN: 2036-7392
2036-7406
08419442
DOI: 10.4081/dr.2022.9418
Popis: Brooke-Spiegler syndrome is a rare disorder, characterized by the development of skin adnexal tumors, including cylindromas, trichoepitheliomas, spiradenomas. Although these neoplasms are benign in most patients, a malignant transformation can rarely occur. Furthermore, an occasional association between cutaneous adnexal tumors and basal cell adenoma as well as adenocarcinoma of the parotid gland has been rarely described, with approximately 20 cases reported. We report a case of BSS presenting with a malignant eccrine spiradenocylindroma, in a patient with previous history of parotid basal cell tumor.
Databáze: Directory of Open Access Journals