Surgical treatment of penoscrotal lymphedema in a patient with Milroy’s disease: case report
| Autor: | João Roberto Farias de Souza, Maria Luiza Marialva Rodrigues, Sérgio Antônio Saldanha Rodrigues Tamborini, Lívia Dornelas Côrrea, Clarissa Leite Turrer, Armando Chiari |
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| Jazyk: | English<br />Portuguese |
| Rok vydání: | 2022 |
| Předmět: | |
| Zdroj: | Revista Brasileira de Cirurgia Plástica, Vol 37, Iss 02, Pp 250-255 (2022) |
| Druh dokumentu: | article |
| ISSN: | 1983-5175 2177-1235 |
| DOI: | 10.5935/2177-1235.2022RBCP0040 |
| Popis: | Introduction: Milroy disease manifests itself as lymphedema of the lower limbs and genital region, which causes physical and social damage. Case Report: A case of severe-scrotal lymphedema in a patient with Milroy disease. Surgical resection of the affected tissue and reconstruction with local flaps and skin graft were performed. Discussion: Milroy disease is a rare autosomal dominant disease. The clinical presentation is progressive and results from hypoplasia of the lymphatic vessels of the lower limbs. Treatment in advanced cases is mainly surgical. Conclusion: In the case of a patient with Milroy disease and severe penoscrotal lymphedema, surgical treatment is a good option. The use of parascrotal flaps for scrotoplasty associated with a graft to recover the penis provides a good functional result. |
| Databáze: | Directory of Open Access Journals |
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