Hereditary angioedema with an acute attack resolved after bone marrow transplantation for acute myeloid leukemia: a case report

Autor: Daisuke Honda, Isao Ohsawa, Masashi Aizawa, Yasuhiko Tomino, Katsuhiko Asanuma
Jazyk: angličtina
Rok vydání: 2023
Předmět:
Zdroj: Allergy, Asthma & Clinical Immunology, Vol 19, Iss 1, Pp 1-4 (2023)
Druh dokumentu: article
ISSN: 1710-1492
DOI: 10.1186/s13223-023-00803-5
Popis: Abstract Background Hereditary angioedema (HAE), which is caused by C1-inhibitor (C1-INH) deficiency or dysfunction, is a rare and potentially life-threatening disease. In patients with HAE, excess production of bradykinin causes acute unpredictable recurrent attacks of angioedema in localized regions, including the larynx and intestines. Given the fact that HAE is an autosomal dominant disease, C1-INH produced in patients with HAE is 50% of that produced in healthy individuals. However, most patients with HAE present plasma C1-INH function of
Databáze: Directory of Open Access Journals
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