Isolated unilateral absence of pulmonary artery (IUAPA) in adults: A case series and review of literature

Autor: Yi Jia Loo, Rajesh Thomas, Lokesh Yagnik
Jazyk: angličtina
Rok vydání: 2023
Předmět:
Zdroj: Respirology Case Reports, Vol 11, Iss 1, Pp n/a-n/a (2023)
Druh dokumentu: article
ISSN: 2051-3380
DOI: 10.1002/rcr2.1073
Popis: Abstract Unilateral Absence of Pulmonary Artery (UAPA) is a rare congenital malformation that is usually associated with cardiac anomalies. When there is no congenital cardiac abnormality it is rarer still and is termed isolated unilateral absence of pulmonary artery (IUAPA) (4). IUAPA may remain undetected until adulthood and frequently found incidentally on imaging for other indications. Symptoms are usually secondary to complications which include pulmonary hypertension, recurrent respiratory tract infections, bronchiectasis and haemoptysis. We report two cases with widely contrasting presentation and trajectories, leading to individualized management strategies.
Databáze: Directory of Open Access Journals
Nepřihlášeným uživatelům se plný text nezobrazuje