Familial Congenital Hepatic Fibrosis: Report of a Family with Three Affected Children

Autor: Fatemeh Farahmand, Khadije Soleimani, Mojtaba Hashemi, Arezoo Shafieyoun, Nima Rezaei, Azizollah Yousefi
Jazyk: angličtina
Rok vydání: 2013
Předmět:
Zdroj: Acta Medica Iranica, Vol 51, Iss 9 (2013)
Druh dokumentu: article
ISSN: 0044-6025
1735-9694
Popis: Congenital hepatic fibrosis (CHF) is a developmental disorder of the biliary system, characterized by defective remodeling of the ductal plate. Herein a family of three children, from consanguineous parents, with minor thalassemia is presented who suffered from congenital hepatic fibrosis (CHF). Prompt diagnosis and appropriate treatment are necessary to avoid further complications in the affected patients.
Databáze: Directory of Open Access Journals