Anatomy, embryology, and imaging of situs ambiguous with polysplenia and left IVC

Autor: Rosa Montero-Macías, MD, David Krief, MD, Vincent Villefranque, MD, Mohamed Kilani, MD, Juan Manuel Castillo-Tuñon, MD, PhD
Jazyk: angličtina
Rok vydání: 2023
Předmět:
Zdroj: Radiology Case Reports, Vol 18, Iss 5, Pp 1727-1732 (2023)
Druh dokumentu: article
ISSN: 1930-0433
DOI: 10.1016/j.radcr.2023.02.005
Popis: The situs ambiguous or heterotaxy syndrome is a type of syndrome that involves multiple visceral abnormalities, vascular ones and associated with left isomerism. Malformation of gastroenterologic system includes polysplenia (segmented spleen or multiple splenules), agenesis (partial or complete) of the dorsal pancreas and anomalous of the inferior vena cava implantation. Here, we describe and show the anatomy of a patient with left side inferior vena cava, situs ambiguous (complete common mesentery), polysplenia, and short pancreas. We also discuss about the embryologic process and the implications of these anomalies during gynecologic, digestive, and liver surgeries.
Databáze: Directory of Open Access Journals