Primary solitary neurofibroma of penis in a child: case report and review

Autor: Mohammad Sohail Ahmad, Santosh Kumar Mahalik, Biswajit Sahoo, Mukund Namdev Sable, Akash Bihari Pati, Kanishka Das
Jazyk: angličtina
Rok vydání: 2022
Předmět:
Zdroj: African Journal of Urology, Vol 28, Iss 1, Pp 1-6 (2022)
Druh dokumentu: article
ISSN: 1110-5704
1961-9987
DOI: 10.1186/s12301-022-00286-7
Popis: Abstract Background Genital involvement in neurofibromas is rare and can involve both the clitoris and penis; in the latter, it usually accompanies a systemic pathology. Isolated penile neurofibroma is anecdotal. This report presents an unusual solitary penile neurofibroma in a child, discusses its surgical management and reviews the literature. Case presentation A 6-year child presented with history of swelling on the undersurface of his penis and obstructive voiding symptoms since 18 months of age. He underwent a partial excision at 5 years of age elsewhere which recurred. The swelling was a 3 × 2 cm, firm, midline, smooth surfaced, longitudinally oblong mass over the ventral penis extending from root to mid shaft with restricted mobility. There was no inguinal lymphadenopathy. Ultrasonography and cystoscopy characterized it to be a corpus spongiosal soft tissue mass encasing and indenting the contained penile urethra. The mass was completely excised along with involved urethra and corpus spongiosa and a penoscrotal urethrostomy created. Histopathological analysis revealed it to be a benign nerve sheath tumor/neurofibroma. He had no stigmata of neurofibromatosis and the ophthalmologic examination was unremarkable. At 2-year follow-up, he is well, has normal glanular sensation and erectile function and awaits urethral reconstruction. Conclusion Primary solitary penile neurofibroma in children is extremely rare. This report details the presentation and management of a ventral penile neurofibroma involving the adjacent urethra/corpora spongiosa.
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