An unusual thoracic localizations of Erdheim- Chester disease: A case report

Autor: C. Massaccesi, S. Colella, F. Fioretti, V. D'Emilio, G. Panella, G. Primomo, F. Barbisan, R. Pela, V. Poletti
Jazyk: angličtina
Rok vydání: 2017
Předmět:
Zdroj: Respiratory Medicine Case Reports, Vol 20, Iss C, Pp 116-119 (2017)
Druh dokumentu: article
ISSN: 2213-0071
DOI: 10.1016/j.rmcr.2017.01.006
Popis: Erdheim- Chester disease is a rare non- Langerhans cell histiocytosis that usually involves the bones, heart, central nervous system, retroperitoneum, eyes, kidneys, skin and adrenals. Lungs are affected in up to one-half cases; at CT scan various patterns are described: interstitial disease, consolidations, micronodules and microcysts, with or without pleural involvement. We presented a case of a 59 year-old man with unusual intrathoracic manifestation of Erdheim- Chester disease. Singularities of our report are the lonely thoracic involvement at the onset of the disease and a histiocytic lesion in the posterior mediastinum.
Databáze: Directory of Open Access Journals