Autor: |
Joshua Y. Chua, MD, Ji Min Ling, FRCS, Derrick W.Q. Lian, FRCPath, Mei Yoke Chan, FRCP, David C.Y. Low, FRCS, Sharon Y.Y. Low, PhD, FRCS |
Jazyk: |
angličtina |
Rok vydání: |
2017 |
Předmět: |
|
Zdroj: |
Interdisciplinary Neurosurgery, Vol 10, Iss , Pp 101-103 (2017) |
Druh dokumentu: |
article |
ISSN: |
2214-7519 |
DOI: |
10.1016/j.inat.2017.07.015 |
Popis: |
Langerhans Cell Histiocytosis is a rare disease featuring aberrant proliferation of dendritic cells that can infiltrate the bony skeleton. The authors report a case of six-year-old female presenting with torticollis. She was found to have extensive lytic LCH lesions in the cranio-cervical junction, causing atlanto-axial rotatory subluxation. Decision was made for a non-surgical approach to treat the patient. She was placed in a Halo brace, and given concomitant chemotherapy. Post-treatment imaging demonstrated near-complete reconstitution of the skeleton affected by LCH. This case highlights the feasibility of non-surgical treatment in selected LCH patients at high-risk of spinal instability. Keywords: Atlanto-axial subluxation, Langerhans cell histocytosis, Torticollis |
Databáze: |
Directory of Open Access Journals |
Externí odkaz: |
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