A Case of Prune Belly Syndrome

Autor: Wei Xu, Hui Wu, Dong-Xuan Wang, Zhi-Hong Mu
Jazyk: angličtina
Rok vydání: 2015
Předmět:
Zdroj: Pediatrics and Neonatology, Vol 56, Iss 3, Pp 193-196 (2015)
Druh dokumentu: article
ISSN: 1875-9572
DOI: 10.1016/j.pedneo.2013.03.014
Popis: Prune belly syndrome (PBS) is a rare congenital disorder characterized by deficient abdominal wall muscles, urinary tract malformation, and, in males, cryptorchidism. We present a case of PBS in China. The patient was a newborn baby boy who had wrinkled, “prune-like” abdominal skin, bilateral cryptorchidism, and urinary system malformation, complicated with hypoplasia of the lung and branch of the coronary artery–right ventricular fistula. His kidney function was inadequate. The patient subsequently died at age 28 days due to septicemia from a severe urinary tract infection.
Databáze: Directory of Open Access Journals