| Autor: |
S. V. Gautier, O. M. Tsirulnikova, D. S. Mnatsakanyan, I. M. Ilyinsky, N. P. Mozheiko |
| Jazyk: |
ruština |
| Rok vydání: |
2013 |
| Předmět: |
|
| Zdroj: |
Vestnik Transplantologii i Iskusstvennyh Organov, Vol 15, Iss 1, Pp 67-74 (2013) |
| Druh dokumentu: |
article |
| ISSN: |
1995-1191 |
| DOI: |
10.15825/1995-1191-2013-1-67-74 |
| Popis: |
Glycogen storage diseases I, III and IV types are congenital disorders, which are commonly associated with severe liver diseases. Liver transplantation has been proposed as a treatment of choise for these disorders. While liver transplantation corrects the primary hepatic enzyme defect, the extrahepatic manifestations of glycogenoses often complicate the posttransplant management. Upon review of the English-language literature, 42 children under 18 years old were discovered to have undergone liver transplantation for complications associated with glycogenoses (18 patients with Ia type, 6 – with Ib type, one patient – with III type, 17 – with IV type). This artic- le represents the pediatric liver transplantation for complications associated with glycogenosis Ia type, analyzed posttransplant period in this recipient. |
| Databáze: |
Directory of Open Access Journals |
| Externí odkaz: |
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