Rare association of hyper IgE syndrome with cervical rib and natal teeth
| Autor: | Roshan Anupama, Janaki C, Parveen B, Gomathy N |
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| Jazyk: | angličtina |
| Rok vydání: | 2009 |
| Předmět: | |
| Zdroj: | Indian Journal of Dermatology, Vol 54, Iss 4, Pp 372-374 (2009) |
| Druh dokumentu: | article |
| ISSN: | 0019-5154 1998-3611 |
| Popis: | Hyper IgE syndrome (HIES) is a rare immunodeficiency syndrome characterized by a triad of cutaneous abscesses, mostly caused by Staphylococus aureus; pneumonia; and raised IgE levels. Nonimmunological associations include course facial features, multiple bone fractures, joint hyperextensibility, and retained primary dentition. Patients require long-term antibiotic therapy. We report here a classical case of HIES with rare associations of natal teeth, bilateral cervical ribs, and conductive deafness. The patient was being treated with monteleukast and dapsone. |
| Databáze: | Directory of Open Access Journals |
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