Management of a Kaposiform haemangioendothelioma of the kidney with Kasabach-Meritt phenomenon without chemotherapy

Autor: Mya Soe Nwe, Marc Weijie Ong, Joyce Ching Mei Lam, Kenneth Tou-En Chang, Marielle V. Fortier, Olivia Wijeweera, Ah Moy Tan, Amos Hong Pheng Loh
Jazyk: angličtina
Rok vydání: 2016
Předmět:
Zdroj: Pediatric Hematology Oncology Journal, Vol 1, Iss 4, Pp 89-92 (2016)
Druh dokumentu: article
ISSN: 2468-1245
DOI: 10.1016/j.phoj.2017.03.001
Popis: Kaposiform haemangioendothelioma (KHE) is a benign vascular tumour. While it is not associated with distant spread, it can be locally aggressive and associated with Kasabach-Merritt syndrome (KMS). There were only 2 prior reports of KHE isolated to the kidney, with both having been managed with neoadjuvant chemotherapy. We present a case report of renal KHE in a paediatric patient managed instead with upfront surgical resection, and discuss the close interdisciplinary diagnostic and management approach undertaken to facilitate this, and the considerations in the approach.
Databáze: Directory of Open Access Journals