Primary Intrarenal Neuroblastoma with Hypertension and Disseminated Intravascular Coagulation

Autor: Bibi Shahin Shamsian, Mohammad Kajizadi, Nima Rezaei, Nozar Ghojehvand, Roxana Azma, Mohsen Rouzrokh, Maryam Kazemi Aghdam, Seyed Malek Mesbah, Farid Ghazizadeh, Mohammad Taghi Arzanian
Jazyk: angličtina
Rok vydání: 2013
Předmět:
Zdroj: Case Reports in Oncological Medicine, Vol 2013 (2013)
Druh dokumentu: article
ISSN: 2090-6706
2090-6714
DOI: 10.1155/2013/684939
Popis: The primary intrarenal neuroblastoma (IRNB) is a rare condition. Intrarenal neuroblastoma typically results from direct renal invasion from an adrenal neuroblastoma, but true intrarenal neuroblastoma originates either sequestered adrenal rests during the fetal life or intrarenal sympathetic ganglia. Clinical, radiological, and pathological correlation is very essential for diagnosis and appropriate management of this type of unusual cases. The distinction of this rare tumor from Wilms’ tumor is an important challenge since both tumors have major differences in prognostic and therapeutic response. We present a 3-year-old boy of primary intrarenal neuroblastoma with extensive abdominal and mediastinal mass, persistent hypertension, and disseminated intravascular coagulation (DIC).
Databáze: Directory of Open Access Journals