Chronic Thromboembolic Pulmonary Hypertension in a Child With Sickle Cell Disease

Autor:	Robert Spencer, Gerson Valencia Villeda, Koji Takeda, Erika B. Rosenzweig
Jazyk:	angličtina
Rok vydání:	2020
Předmět:	pediatric cardiology pulmonary hypertension CTEPH—chronic thromboembolic pulmonary hypertension sickle cell disease hematology Pediatrics RJ1-570
Zdroj:	Frontiers in Pediatrics, Vol 8 (2020)
Druh dokumentu:	article
ISSN:	2296-2360 91797047
DOI:	10.3389/fped.2020.00363
Popis:	Chronic thromboembolic pulmonary hypertension is a potentially curable form of pre-capillary pulmonary hypertension (PH) resulting from incomplete resolution of pulmonary thromboemboli. We describe an 11-year-old boy with homozygous sickle cell disease with an indwelling catheter found to have severe PH on routine screening echocardiography. The diagnosis was confirmed by CT, ventilation-perfusion scintigraphy, and right heart catheterization. The patient was medically managed until undergoing pulmonary thromboendarterectomy with resolution of his PH. This case highlights the need for pediatric providers to be aware of this underdiagnosed form of PH, particularly for patients at high risk.
Databáze:	Directory of Open Access Journals
Externí odkaz:	https://doaj.org/article/4e9c01ea2aa1432f9179704726ac8ed2 Zobrazit plný text záznamu View record in DOAJ