| Autor: |
Sahana Somasegar, Lisa Han, Aaron Miller, Pankhuri Wanjari, Peng Wang, Jennifer A. Bennett, S. Diane Yamada |
| Jazyk: |
angličtina |
| Rok vydání: |
2021 |
| Předmět: |
|
| Zdroj: |
Gynecologic Oncology Reports, Vol 36, Iss , Pp 100752- (2021) |
| Druh dokumentu: |
article |
| ISSN: |
2352-5789 |
| DOI: |
10.1016/j.gore.2021.100752 |
| Popis: |
Cowden syndrome is a rare hereditary cancer syndrome characterized by a germline PTEN mutation which results in an increased risk of developing breast, thyroid, and endometrial carcinoma, as well as widespread benign hamartomas. Phyllodes tumor (PT) is a rare fibroepithelial tumor that accounts for less than 1% of all breast tumors. As mammary-type glands can be found in the anogenital region, PTs can rarely arise in this location. We describe the presentation, workup and management of a PT of the vulva that developed in a patient with Cowden syndrome. This report represents the first time a vulvar PT has been described in association with Cowden syndrome and should be considered in the differential diagnosis of a slow-growing vulvar mass. |
| Databáze: |
Directory of Open Access Journals |
| Externí odkaz: |
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