A multidisciplinary approach to sphenoid wing dysplasia presenting with pulsatile proptosis in neurofibromatosis Type 1: A rare case report

Autor:	S Prathibha, Vandana Parasar, S Yasmin, V V Seetha Pramila
Jazyk:	angličtina
Rok vydání:	2018
Předmět:	Lisch nodule neurofibroma neurofibromatosis pulsatile proptosis sphenoid wing dysplasia Ophthalmology RE1-994
Zdroj:	Indian Journal of Ophthalmology, Vol 66, Iss 1, Pp 157-160 (2018)
Druh dokumentu:	article
ISSN:	0301-4738 1998-3689
DOI:	10.4103/ijo.IJO_429_17
Popis:	Neurofibromatosis (NF) with sphenoid wing dysplasia is a rare clinical entity. Herewith, we present a case of NF with sphenoid wing dysplasia which presented with pulsatile progressive proptosis. Other ocular symptoms or visual disturbances were absent. Diagnosis of the condition was not easy and the management was a challenging task which needed multidisciplinary approach as there were ocular, neurological, orthopedic, and dermatological manifestations. With neurosurgical intervention, reconstruction of the sphenoid wing was possible. Proptosis was corrected without any disturbance of vision.
Databáze:	Directory of Open Access Journals
Externí odkaz:	https://doaj.org/article/4d9fa351d1024c83a0e35b005388c55d Zobrazit plný text záznamu View record in DOAJ Plný text ve formátu PDF