Disseminated granuloma annulare-like presentation of juvenile Wells' syndrome

Autor: Celestin Kouadio Ahogo, I P Gbery, B Vagamon, A Fauconneau
Jazyk: angličtina
Rok vydání: 2017
Předmět:
Zdroj: Indian Journal of Paediatric Dermatology, Vol 18, Iss 2, Pp 110-112 (2017)
Druh dokumentu: article
ISSN: 2319-7250
DOI: 10.4103/2319-7250.203002
Popis: A 5-year-old boy was referred because of urticarial flares with angioedema. Antihistamines and systemic steroids were not useful to prevent flares. At examination, at distance of a flare, chronic red-brownish plaques were found on the legs, trunk, and back, resembling granuloma annulare. The skin biopsy showed epithelioid and giant-cell granulomas, elastophagia, and “flames figures” surrounded with many eosinophils. A diagnosis of disseminated granuloma annulare-like variant of Wells' syndrome as described earlier by Caputo was made. A treatment with dapsone was initiated and enabled to stop flares. Wells' syndrome is a rare clinicopathologic entity with a chronic benign course and often misleading clinical presentation. Our case illustrates the clinical polymorphism and benefit of dapsone therapy.
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