| Autor: |
Masato Kono, Yutaro Nakamura, Yoshiyuki Oyama, Go Saito, Yu Koyanagi, Koichi Miyashita, Akari Tsutsumi, Yasunori Enomoto, Takeshi Kobayashi, Yoshihiro Miki, Dai Hashimoto, Noriyuki Enomoto, Thomas V. Colby, Takafumi Suda, Hidenori Nakamura |
| Jazyk: |
angličtina |
| Rok vydání: |
2018 |
| Předmět: |
|
| Zdroj: |
Respiratory Medicine Case Reports, Vol 25, Iss , Pp 257-260 (2018) |
| Druh dokumentu: |
article |
| ISSN: |
2213-0071 |
| DOI: |
10.1016/j.rmcr.2018.09.017 |
| Popis: |
A 64-year-old man was admitted to our hospital with an abnormal chest shadow. The patient was a current-smoker and had a past illness of autoimmune pancreatitis with a high serum level of IgG4, 348 mg/dL. Chest CT showed upper-lobe emphysema, and lower-lobe reticulation with honeycombing, suggestive of combined pulmonary fibrosis with emphysema (CPFE). Surgical lung biopsy was revealed a usual interstitial pneumonia pattern with marked infiltration of IgG4-positive plasma cells. The patient was diagnosed with IgG4 related disease (IgG4-RD) presenting with CPFE. Pulmonary manifestation was improved by corticosteroid therapy. IgG4-RD may be an underlying condition in patient with CPFE. Keywords: Combined pulmonary fibrosis and emphysema (CPFE), IgG4-related disease (IgG4-RD), Usual interstitial pneumonia (UIP) |
| Databáze: |
Directory of Open Access Journals |
| Externí odkaz: |
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