Erdheim–Chester Disease Involving the Biliary System and Mimicking Immunoglobulin G4-Related Disease: A Case Report

Autor: Hyuk Gi Hong, Yong Eun Chung, June Park, Yeo Eun Kim
Jazyk: English<br />Korean
Rok vydání: 2023
Předmět:
Zdroj: Journal of the Korean Society of Radiology, Vol 84, Iss 3, Pp 757-762 (2023)
Druh dokumentu: article
ISSN: 2951-0805
DOI: 10.3348/jksr.2022.0114
Popis: First described in 1930 as a lipoid granulomatosis, Erdheim-Chester disease (ECD) is a rare histiocytosis encompassing a group of disorders caused by overproduction of histiocytes, a subtype of white blood cells. This disease most commonly involves the bones and can affect organs in the abdomen; however, biliary involvement is rarely reported. We report a case of ECD with biliary involvement, which rendered it difficult to radiologically distinguish ECD from immunoglobulin G4-related disease.
Databáze: Directory of Open Access Journals