Fibrosing arthropathy in juvenile scleroderma

Autor: D. A. Dibrov, M. N. Starovoitova, O. V. Desinova
Jazyk: ruština
Rok vydání: 2021
Předmět:
Zdroj: Современная ревматология, Vol 15, Iss 2, Pp 64-68 (2021)
Druh dokumentu: article
ISSN: 1996-7012
2310-158X
DOI: 10.14412/1996-7012-2021-2-64-68
Popis: The group of scleroderma diseases includes a number of clinical entities, the main symptom of which is skin tightening. Scleroderma is a prominent example of these diseases, characterized by excessive synthesis and deposition of collagen in organs and tissues. A patient with juvenile systemic scleroderma with induration of the skin and underlying tissues, and persistent contractures of large joints since childhood, is described. This clinical example illustrates disease course peculiarities and differential diagnosis of systemic and limited (focal) scleroderma and scleroderma-like conditions in pediatric patients. The feasibility of pathogenetic therapy aimed at improving patient's the quality of life with formed disease phenotype is shown.
Databáze: Directory of Open Access Journals