Plexogenic pulmonary hypertension associated with POEMS syndrome

Autor: Thomas Czeczok, Peter Lin, Eunhee Yi
Jazyk: angličtina
Rok vydání: 2017
Předmět:
Zdroj: Respiratory Medicine Case Reports, Vol 22, Iss C, Pp 168-170 (2017)
Druh dokumentu: article
ISSN: 2213-0071
DOI: 10.1016/j.rmcr.2017.08.011
Popis: Pulmonary hypertension is one of the well-known clinical manifestations of polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes (POEMS) syndrome, occurring in approximately 25–30% of the affected individuals. However, the histopathologic spectrum of pulmonary hypertension associated with POEMS syndrome has not been fully documented in the literature. Herein, we report an autopsy case of POEMS syndrome in a patient whose lung tissues showed histopathology indistinguishable from that of idiopathic pulmonary arterial hypertension with abundant plexiform lesions in the small pulmonary arteries.
Databáze: Directory of Open Access Journals