Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease

Autor: Luana Vieira Mukamal, Celso Tavares Sodré, Lara Beatriz Prata, Fernanda Nakasato, Tullia Cuzzi, Marcia Ramos-e-Silva
Jazyk: angličtina
Rok vydání: 2018
Předmět:
Zdroj: Case Reports in Dermatology, Vol 10, Iss 2, Pp 175-181 (2018)
Druh dokumentu: article
ISSN: 1662-6567
DOI: 10.1159/000489162
Popis: The authors present a classic case of Churg-Strauss syndrome with an exuberant clinical picture in a 34-year-old woman. She showed the following diagnostic criteria: asthma, polyneuropathy, rhinopathy, marked eosinophilia, positive p-ANCA with a perinuclear pattern, and skin histopathology results suggestive of vasculitis with eosinophils. There was a good response to prednisone, dexamethasone pulse therapy, and cyclophosphamide.
Databáze: Directory of Open Access Journals