Therapeutic approach of a pancreatic Ewing Sarcoma/PNET: case report and literature review
| Autor: | Rodrigo Nascimento Pinheiro, Fabiane Kellem Oliveira dos Santos Cesário, José Pablo Mata Mondragon, Fábio Daniel Barbosa da Silva, Renata Pereira Fontoura, José Donato de Sousa, Carlos Henrique de Aguiar Botelho |
|---|---|
| Jazyk: | angličtina |
| Rok vydání: | 2020 |
| Předmět: |
Neuroectodermal tumors
Primitive Peripheral Sarcoma Ewing Pancreatic neoplasms Combined modality therapy Quality of life Tumores neuroectodérmicos primitivos periféricos Neoplasias pancreáticas Terapia de modalidade combinada Qualidade de vida Neoplasms. Tumors. Oncology. Including cancer and carcinogens RC254-282 Medicine |
| Zdroj: | Brazilian Journal of Oncology, Vol 16, Iss (2020) |
| Druh dokumentu: | article |
| ISSN: | 2526-8732 |
| DOI: | 10.5935/2526-8732.20200020 |
| Popis: | Peripheral primitive neuroectodermal tumors (pPNETs) are part of the Ewing sarcoma family. A few more than 30 cases of pPNETs originating on the pancreas have been reported in the consulted literature. We report a locally advanced pancreatic pPNET, with the longest follow-up and survival in the consulted literature, considering quality of life outcomes. 22-year-old male patient, with a pancreatic pPNET comprising pancreatic body and tail with gastric invasion. He underwent multi organic resection and adjuvant chemotherapy and radiotherapy. After 8 years of follow-up, he was free of disease and with a good quality of life self-evaluation. The aggressive surgical approach associated with multimodal regimens provided improvement in disease-free survival and a positive impact on quality of life. |
| Databáze: | Directory of Open Access Journals |
| Externí odkaz: |
|