Perivascular Epithelioid Cell Tumour with Intraorbital Location: Report of a Case and Review of the Literature

Autor: Idania Lubo, Ileana Fermín, Olindo Massarelli, Roberta Gobbi, Paolo Cossu Rocca
Jazyk: angličtina
Rok vydání: 2016
Předmět:
Zdroj: Case Reports in Pathology, Vol 2016 (2016)
Druh dokumentu: article
ISSN: 2090-6781
2090-679X
DOI: 10.1155/2016/1936421
Popis: The Perivascular Epithelioid Cell tumours (PEComas) are rare mesenchymal neoplasms recognized as entity by the World Health Organization. The tumour cells have an uncertain origin and are characterized by distinctive histological and immunohistochemical features. We report a case of PEComa occurring as intraorbital lesion in a 47-year-old man. We found only two other cases described in the literature and we considered all three cases together in order of histology, immunohistochemistry, and clinical outcome. We found a strict histological overlapping and quite similar immunohistological results. All three cases showed a favourable clinical course probably related to small size of tumours (
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