Pulmonary capillary hemangiomatosis: An unusual cause of primary pulmonary hypertension in a child with characteristic computed tomography imaging features

Autor:	D Manjubashini, K Nagarajan, B Rajesh Kumar
Jazyk:	angličtina
Rok vydání:	2019
Předmět:	Multidetector computed tomography primary pulmonary hypertension pulmonary capillary hemangiomatosis Diseases of the respiratory system RC705-779
Zdroj:	Lung India, Vol 36, Iss 2, Pp 157-159 (2019)
Druh dokumentu:	article
ISSN:	0970-2113 0974-598X
DOI:	10.4103/lungindia.lungindia_122_18
Popis:	Pulmonary capillary hemangiomatosis (PCH) is a rare cause of primary pulmonary hypertension (PPH) diagnosed in children and young adults with a nonspecific clinical presentation of dyspnea, cough, chest pain, and fatigue. It is characterized by extensive proliferation of pulmonary capillaries within alveolar septa. The imaging features include diffuse centrilobular ground-glass opacities with features of pulmonary hypertension. We present a case of PCH in an 11-year-old boy who was diagnosed with PPH in echocardiography and referred for diagnostic imaging.
Databáze:	Directory of Open Access Journals
Externí odkaz:	https://doaj.org/article/3ce9b0b1a44c470fb666b6b7474e7678 Zobrazit plný text záznamu View record in DOAJ Plný text ve formátu PDF