Pulmonary hypertension associated with congenital heart disease; clinical decision scenario

Autor: Ali A. Alakhfash, Abdullah Alqwaiee, Ghadeer Ali Alakhfash, Athkar Alhajjaj, Abdulrahman A. Almesned
Jazyk: angličtina
Rok vydání: 2020
Předmět:
Zdroj: Respiratory Medicine Case Reports, Vol 31, Iss , Pp 101286- (2020)
Druh dokumentu: article
ISSN: 2213-0071
DOI: 10.1016/j.rmcr.2020.101286
Popis: Pulmonary arterial hypertension associated with congenital heart disease (PAH-CHD) is one type under group 1 PH. Undiagnosed or delayed diagnosis of significant CHD might lead to significant PAH and at the end might lead to Eisenmenger syndrome. We could expect the degree of PAH in patients with CHD by proper clinical assessment as well as by the basic assessment tools including the chest x-ray (CXR), ECG, and transthoracic echocardiography (TTE).We are presenting a three and half years old child with a delayed/missed diagnosis of large patent ductus arteries (PDA) who present with significant PAH. Clinical evaluation, CXR, ECG, TTE, as well as cardiac catheterization data are presented, with a review of the current guidelines regarding the management of pediatric patients with PAH-CHD.
Databáze: Directory of Open Access Journals